Darras, Basil, Miller, Patricia, Snyder, Brian, and Troy, Michael
Beschreibung:
Spinal muscular atrophy (SMA) consists of a group of neuromuscular disorders characterized by degeneration of alpha motor neurons, leading to a lower motor neuron-type syndrome. Children afflicted with SMA 1 and 2 are prone to...
Graham, Robert, Miller, Patricia, Snyder, Brian, and Troy, Michael
Beschreibung:
Context: Children with SMA suffer from scoliosis, global weakness, and Thoracic Insufficiency (TIS). Normalized pulmonary function tests are inadequate when evaluating these patients for improvement in PFTs. Objective: Forced...